Int J Clin Pract 2000 04, 54: 3, 171-9
Abstract: Cystic fibrosis (CF) is one of the commonest lethal inherited conditions among Caucasians. It affects multiple organ systems and exhibits a range of clinical problems of varying severity. Life expectancy has improved in recent years as treatment regimes have become more intensive, but current treatments are expensive, often time consuming and may affect quality of life. This review summarizes the treatments currently used in the management of patients with CF, and the evidence for these.