Cystic Fibrosis Articles
Energy Metabolism During Anaerobic Exercise in Children with Cystic Fibrosis and Asthma
BOAS SR, DANDURAN MJ, MCCOLLEY SA MEDICINE AND SCIENCE IN SPORTS AND EXERCISE 1999 SEP ;31(9):1242-9 ABSTRACT: Purpose: The nature of a child’s daily physical activity requires both aerobic and anaerobic energy metabolism. Aerobic exercise becomes compromised with...
Therapy for Cystic Fibrosis
LUDER, E Gene TOPICS IN CLINICAL NUTRITION 1999 SEP ;14(4):22-30 ABSTRACT: Cystic fibrosis (CF) is a common genetic disorder in the Caucasian population. The gen was identified in 1989 on chromosome 7. The encoded gene product, named cystic fibrosis transmembrane...
Effect of Glucose to Fat Ratio on Energy Substrate Disposal in Children with Cystic Fibrosis Fed Enterally
ATEGBO S, DABADIE A, DRUON D, GOTTRAND F, HANKARD R, MICHAUD L, TURCK D CLINICAL NUTRITION 1999 OCT: 18(5):297-300 ABSTRACT: High fat containing diets lower VCO2 in patients with impaired pulmonary function fed at a high level of energy intake. We tested the effect...
Physiological and Psychosocial Contributors to Malnutrition in Children with Cystic Fibrosis: Review
ANTHONY H, CATTO-SMITH A, PAXTON S, PHELAN P CLINICAL NUTRITION 1999 DEC;18(6): 327-35 ABSTRACT: Malnutrition was once thought to be an inevitable consequence of cystic fibrosis (CF). It is now considered preventable but still contributes considerable morbidity in...
When should hyperglycemia be treated in cystic fibrosis? [letter]
Cotellessa M, Minicucci L, Lorini R J Pediatr 2000 05, 136: 5, 706-7
Home-based exercise programs in cystic fibrosis: are they worth it? [editorial; comment]
Bar Or O J Pediatr 2000 03, 136: 3, 279-80
Interleukin-1beta regulates CFTR expression in human intestinal T84 cells
Cafferata EG, Gonzalez Guerrico AM, Giordano L, Pivetta OH Biochim Biophys Acta 2000 00, 1500: 2, 241-8 Abstract: Cystic fibrosis is an autosomal recessive genetic disease, produced by a mutation in the CFTR gene that impairs its function as a chloride channel. In...
Fat absorption in cystic fibrosis after correction of hypokalaemia [letter]
Hunter I, Stewart L, Mukhopadhyay S Lancet 2000 00, 355: 9207, 900 Abstract: Extracellular potassium up-regulates exocrine pancreatic function in tissue preparations of mammalian pancreatic lobules. We report on a child with cystic fibrosis in whom clinical evidence...
Targeting the urokinase plasminogen activator receptor enhances gene transfer to human airway epithelia.
Drapkin PT, ORiordan CR, Yi SM, Chiorini JA, Cardella J, Zabner J, Welsh MJ J Clin Invest 2000 03, 105: 5, 589-96 Abstract: Developing gene therapy for cystic fibrosis has been hindered by limited binding and endocytosis of vectors by human airway epithelia. Here we...
A randomized controlled trial of a 3-year home exercise program in cystic fibrosis
Schneiderman Walker J, Pollock SL, Corey M, Wilkes DD, Canny GJ, Pedder L, Reisman JJ J Pediatr 2000 03, 136: 3, 304-10 Abstract: OBJECTIVES: To evaluate the effects of a 3-year home exercise program on pulmonary function and exercise tolerance in mildly to...